Abstract
Acquired Lymphangioma circumscriptum is among the rarest and most benign conditions of the lymphatic system. The etiology of L. circumscriptum is unclear. A case is presented involving a 42-year-old Para 4 women diagnosed with acquired L. circumscriptum after presenting with vulvar swelling, for which a simple partial vulvectomy was performed. The clinical presentation of a patient with acquired vulvar L. circumscriptum may resemble that of genital warts and malignancies. Therefore, vulvar lymphangioma should be considered as a differential diagnosis for vulvar swelling. Simple partial vulvectomy is one management option if sclerotherapy and vaporization with CO2 are not available.
Key words: Vulvar swelling, acquired vulvar Lymphangioma circumscriptum, simple partial vulvectomy, case report.