Abstract

Job’s syndrome is an immunodeficiency disorder with defect in leukocyte chemotaxis in some patients. It is also called hyper IgE recurrent infection syndrome. Major manifestations are pruritic dermatitis, recurrent Staphylococcal pneumonias, mucocutaneous candidiasis, restrictive lung disease, scoliosis with other various features. A 20 year old boy who was presented to us with heart failure, abdominal pain and pyoderma was later diagnosed as having job’s syndrome and tuberculosis.

Key words: Job’s syndrome, hyper immunoglobin E syndrome, Buckly syndrome, immunodeficiency.