Abstract

Persistent Müllerian Duct syndrome (PMDS) is a rare variety of male pseudo-hermaphroditism. It is characterized by the persistence of the uterus, fallopian tubes and upper vagina in otherwise normally virilized boys. The association of the syndrome called transverse testicular ectopia (TTE), a condition in which both testes are located in one inguinal canal is rare. Here, we report a young male patient presented with infertility, left sided inguinal hernia and right-sided undescended testis since birth, finally found to have PMDS with TTE.

Key words: Müllerian duct, testicular ectopia, undescended testis, orchidopexy.